Bourebaba N, Kornicka-Garbowska K, Marycz K, Bourebaba L, Kowalczuk A
doi: 10.2174/0929867329666220801161536
ACS Nano 8 , 47714781 (2014)
LCL161, an Oral Smac Mimetic/IAP Antagonist for Patients with Myelofibrosis (MF): Novel Translational Findings Among Long-Term Responders in a Phase 2 Clinical Trial
Primary Carnitine Deficiency Syndromes Two distinct carnitine deficiency states have been reported although a rigid distinction between "primary" and "secondary" carnitine deficiency is difficult to establish in some cases [10]
It depends on both copper and zinc as cofactors, but only copper regulates its activity ( 2 O 2 , CuZn-SODs activity is suppressed, via oxidation of His-118 to form 2-oxo-histidine (Uchida and Kawakishi, 1994)